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Draft Version
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ICD-9 CODES FOR PRIMARY TUMOR, METASTASIS AND SYNDROMES
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CARCINOID PRIMARY SITES
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FOREGUT
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Malignant
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Benign
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Uncertain Behavior
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Unspecified
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Duodenum
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152.0
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211.2
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235.2
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239.0
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Lung-Bronchus
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162.9
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212.3
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235.7
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239.1
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Stomach
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151.9
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211.1
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235.2
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239.0
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Ovary
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183.0
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220
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236.2
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239.5
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Thymus
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164.0
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212.6
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235.8
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239.8
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MIDGUT
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Malignant
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Benign
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Uncertain Behavior
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Unspecified
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Appendix
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153.5
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211.3
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235.2
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239.0
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Colon
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154.0
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211.4
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235.2
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239.0
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Ileum
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152.0
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211.2
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235.2
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239.0
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Jejunum
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152.1
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211.2
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235.2
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239.0
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HINDGUT
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Malignant
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Benign
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Uncertain Behavior
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Unspecified
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Rectum
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154.1
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211.4
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235.2
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239.0
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METASTASIS SITES
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Malignant
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Supraclavicular
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196.0
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Abdominal
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196.2
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Mediastinal
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196.1
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Retroperitoneal
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196.2
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Liver
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197.7
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Bone
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198.5
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Lung
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162.0
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Brain
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198.3
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SYNDROME: CARCINOID SYNDROME - 259.2
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ISLET CELL PRIMARY SITES
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Malignant
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Benign
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Uncertain Behavior
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Unspecified
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Ampulla
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156.2
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211.5
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235.3
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239.0
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Duodenum
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152.0
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211.2
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235.2
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239.0
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Jejunum
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152.1
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211.2
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235.2
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239.0
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Pancreas
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157.9
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211.6
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235.5
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239.0
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Body
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157.1
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211.6
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235.5
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239.0
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Head
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157.0
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211.6
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235.5
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239.0
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Islet Cell
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157.4
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211.7
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235.5
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239.0
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Neck
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157.8
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211.6
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235.5
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239.0
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Tail
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157.2
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211.6
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235.5
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239.0
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METASTASIS SITES
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Malignant
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Supraclavicular
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196.0
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Abdominal
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196.2
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Mediastinal
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196.1
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Retroperitoneal
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196.2
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Liver
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197.7
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Bone
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198.5
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Lung
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162.0
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Brain
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193.8
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SYNDROMES:
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MALIGNANT NEOPLASM OF THE PANCREAS, PRODUCING INSULIN, SOMATOSTATIN OR GLUCAGON, ISLETS OF LANGERHANS
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157.4
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ZOLLINGER-ELLISON SYNDROME
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251.5
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WHIPPLE’S SYNDROME
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040.2
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SWEET’S SYNDROME
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695.89
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MEN-I
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258.0
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Reprinted with permission of Dr. Eugene Woltering
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© This website is copyrighted by NAAPNET 2005 & following — http://www.naapnet.org
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